Although this strategy turned out to be successful, proactive monitoring for the development of ductal stent stenosis during follow-up after the hybrid procedure remains crucial to prevent hemodynamic complications such as cardiac failure and systemic hypoperfusion. Interrupted aortic arch (IAA) is an uncommon congenital cardiovascular malformation characterized by the lack of continuity between the ascending and descending thoracic aorta as described by Steidele in 1778. Three smaller blood vessels branch off the aorta to supply the head and arms with oxygen-rich blood, while the. The aorta rises upwards out of the heart, then curves down to the body (aortic arch). Emphasis is placed on diagnostic assessment and surgical decision making in the presence of varying degrees of left ventricular outflow tract obstruction. As a means to avoid high-risk neonatal surgery in this patient, we pursued a strategy of delayed biventricular repair involving initial hybrid Norwood palliation followed by a Yasui-type operation at 3 months. Interrupted aortic arch is when the large blood vessel that takes blood away from the heart to the rest of the body (aorta) is not fully developed. This chapter summarizes the anatomy, biology, pathophysiology, surgical treatment, and outcomes in patients with interrupted aortic arch and ventricular septal defect. IAA is classi ed into types depending on the aortic arch segment involved. It accounts for less than 2 of congenital heart anomalies. Focal CoA classically presents with signi cant narrowing at the level of the isthmus. Here, we report the case of a patient with 22q11.2 deletion syndrome and a diagnosis of interrupted aortic arch type B2, ventricular septal defect and left ventricular outflow tract obstruction. Interrupted aortic arch is caused by the defective development of the aorta during early fetal life, probably within the first 5-7 weeks. The initial echocardiogram showed a congenital interrupted aortic arch type A, patent ductus arteriosus, and ventricular septal defect. IAA is frequently associated with ventricular septal defects (VSD) and a bicuspid aortic valve. However, each of these procedures carries a high mortality risk, especially in syndromic neonates. Interrupted aortic arch (IAA) is a congenital anomaly where there is interruption or discontinuation of a segment of the aortic arch. Often, the right subclavian artery is aberrant, meaning it arises abnor- mally from the descending aorta. Several options have been proposed, including neonatal Yasui or Ross-Konno operation. In patients with critical left ventricular outflow tract obstruction but adequately sized ventricles, the treatment of choice is biventricular repair.
0 Comments
Leave a Reply. |
AuthorWrite something about yourself. No need to be fancy, just an overview. ArchivesCategories |